Plasminogen Deficiency


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21.       Hidayat AA, Riddle PJ. Ligneous conjunctivitis. A clinicopathologic study of 17 cases. Ophthalmology 1987;94:949-59.

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25.       Cohen J, Cohen S, Cymberknoh MC, Gross M, Hirshoren N, Shoseyov D. Laryngeal obstruction in congenital plasminogen deficiency. Pediatric Pulmonology 2012;47:923-5.

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27.       Pantanowitz L, Bauer K, Tefs K, et al. Ligneous (pseudomembranous) inflammation involving the female genital tract associated with type-1 plasminogen deficiency. International Journal of Gynecological Pathology 2004;23:292-5.

28.       Pantanowitz L. Ligneous cervicitis. BJOG 2004;111:635.

29.       Veres G, Korponay-Szabo I, Maka E, et al. Duodenal ulceration in a patient with celiac disease and plasminogen I deficiency: coincidence or cofactors? Pediatrics 2011;128:e1302-6.

30.       Oskay T, Erdem C, Anadolu R, Peksan Y, Ozsoy N, Gul N. Juvenile colloid milium associated with conjunctival and gingival involvement. J Am Acad Dermatol 2003;49:1185-8.

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34.       De Cock R, Ficker LA, Dart JG, Garner A, Wright P. Topical heparin in the treatment of ligneous conjunctivitis. Ophthalmology 1995;102:1654-9.

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36.       Teresa Sartori M, Saggiorato G, Pellati D, et al. Contraceptive pills induce an improvement in congenital hypoplasminogenemia in two unrelated patients with ligneous conjunctivitis. Thromb Haemost 2003;90:86-91.

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40.       Schott D, Dempfle CE, Beck P, et al. Therapy with a purified plasminogen concentrate in an infant with ligneous conjunctivitis and homozygous plasminogen deficiency. N Engl J Med 1998;339:1679-86.

41.       Watts P, Suresh P, Mezer E, et al. Effective treatment of ligneous conjunctivitis with topical plasminogen. American Journal of Ophthalmology 2002;133:451-5.

42.       Heidemann DG, Williams GA, Hartzer M, Ohanian A, Citron ME. Treatment of ligneous conjunctivitis with topical plasmin and topical plasminogen. Cornea 2003;22:760-2.

43.       Pergantou H, Likaki D, Fotopoulou M, Katsarou O, Xafaki P, Platokouki H. Management of ligneous conjunctivitis in a child with plasminogen deficiency. Eur J Pediatr 2011;170:1333-6.